An unusual case of Ebstein anomaly in 72 year old woman

Background Ebstein’s anomaly is a rare congenital heart disorder (1 per 200,000 live births), accounting for about 0.3 to 0.7% of all cases of congenital heart disease. The condition is characterized by tricuspid valve abnormality with apical displacement of the septal and posterior leaflets from the atrioventricular annulus into the right ventricle, leading to the ‘atrialization’ of a portion of the right ventricle. Only 5% of patients with Ebstein’s anomaly survive beyond the fifth decade while original presentation in older patients is rare.